Catecholaminergic polymorphic ventricular tachycardia
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Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a condition characterised by an abnormal heart rhythm (arrhythmia). As the heart rate increases in response to physical activity or emotional stress, it can trigger an abnormally fast heartbeat called ventricular tachycardia. Episodes of ventricular tachycardia can cause light-headedness, dizziness, and fainting (syncope). In people with CPVT, these episodes typically begin in childhood.
Descrizione
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a condition characterised by an abnormal heart rhythm (arrhythmia). As the heart rate increases in response to physical activity or emotional stress, it can trigger an abnormally fast heartbeat called ventricular tachycardia. Episodes of ventricular tachycardia can cause light-headedness, dizziness, and fainting (syncope). In people with CPVT, these episodes typically begin in childhood.
If CPVT is not recognized and treated, an episode of ventricular tachycardia may cause the heart to stop beating (cardiac arrest), leading to sudden death. Researchers suspect that CPVT may be a significant cause of sudden death in children and young adults without recognized heart abnormalities.
Modelli di ereditarietà
The source lists the following possible inheritance patterns: Autosomal dominant; Autosomal recessive. More than one pattern can apply in different cases.
Related genes
Altri nomi
Bidirectional tachycardia induced by catecholamines
Catecholamine-induced polymorphic ventricular tachycardia
CPVT
Familial polymorphic ventricular tachycardia
FPVT
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Ulteriori letture e riferimenti
- Catecholaminergic polymorphic ventricular tachycardia; MedlinePlus, National Library of Medicine.
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